ABSTRACT

Neural tube defects (NTDs) are multifactorial midline abnormalities that occur during the neurulation process in embryogenesis. Myelomeningocele is an important abnormality that may indicate the necessity of an emergency intervention. Although myelomeningocele can be seen throughout the all spinal axis, the areas with the most common and least common localizations are the lumbosacral region and thoracic region, respectively. The most common co-abnormalities have been reported to be hydrocephalus and Chiari type 2 malformations. There are some differences in the management regarding to the order and the timing of the surgery in myelomeningocele associated with hydrocephalus and Chiari malformations. Here we discuss our management of a rare case of thoracic myelonmeningocele associated with hydrocephalus and Chiari type 2 malformation.

Keywords: Myelomeningocele, hydrocephalus, Chiari malformation type 2, spina bifida