ABSTRACT
Plasmacytoid urothelial carcinoma is a relatively rare form of urothelial transitional cell carcinoma, which primarily presents in the bladder. A cautionary approach is required by the pathologist for the final histologic diagnosis. Since the diagnosis is usually challenging, most cases are diagnosed as metastases in the advanced stage. No clear protocol exists in the urology guidelines as a treatment because there are few data present regarding the disease. In the present study, we aimed to present a case of ureteral plasmacytoid variant of urothelial carcinoma, which to our knowledge is the first to appear in the literature.